Archives of the Turkish Society of Cardiology
Case report of a rarely seen long-segment middle aortic syndrome [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. 2017; 45(2): 181-183 | DOI: 10.5543/tkda.2016.64606

Case report of a rarely seen long-segment middle aortic syndrome

Kahraman Yakut, Ilkay Erdogan
Department Of Pediatric Cardiology, Baskent University, Ankara, Turkey

Middle aortic syndrome (MAS) follows a course with distal thoracic and abdominal aorta stenosis. It is a rare disease that is usually diagnosed after the first decade of life. Clinical reflection of MAS is often in the form of hypertension and claudication in the lower extremities. Its etiology is unclear, but is known to be associated with congenital or acquired diseases. This pathology, which is accompanied by malignant hypertension, often does not respond to medical treatment. In patients with MAS, surgical treatment is first line recommendation to prevent complications such as hypertension, heart failure, intracranial bleeding, or aortic rupture. In order to draw attention to this disease, presently described is case of high blood pressure detected during routine examination of a child who had no complaint, and discovery of long-segment stenosis in the abdominal aorta identified with echocardiography and conventional angiography.

Keywords: Coarctation, congenital heart disease, hypertension, middle aortic syndrome.





How to cite this article
Kahraman Yakut, Ilkay Erdogan. Case report of a rarely seen long-segment middle aortic syndrome. Turk Kardiyol Dern Ars. 2017; 45(2): 181-183

Corresponding Author: Kahraman Yakut, Türkiye
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