ISSN 1016-5169 | E-ISSN 1308-4488
Archives of the Turkish Society of Cardiology
A rare cause of recurrent wheezing and respiratory distress: Scimitar syndrome [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. 2011; 39(7): 595-598 | DOI: 10.5543/tkda.2011.01581

A rare cause of recurrent wheezing and respiratory distress: Scimitar syndrome

Yakup Ergül1, Kemal Nişli1, Nermin Güler2, Ümrah Aydoğan1
1Division of Pediatric Cardiology, Department of Pediatrics, Istanbul University, Istanbul Faculty Of Medicine, Istanbul, Turkey
2Division of Pediatric Allergy And Chest Diseases, Department of Pediatrics, Istanbul University, Istanbul Faculty of Medicine, Istanbul, Turkey

Scimitar syndrome is characterized by partial or total anomalous pulmonary venous return from the right lung. We present a 15-month-old boy who was diagnosed with Scimitar syndrome after examinations for recurrent wheezing and respiratory distress. The chest radiograph showed a scimitar sign in the right hemithorax, obscuring the contours of the right atrium. Echocardiography showed dilatation of the right heart cavities and increased flow in the inferior vena cava, without a cardiac abnormality. The patient underwent cardiac catheterization for radiographic and hemodynamic evaluations, during which a scimitar vein was detected, draining the right pulmonary veins to the inferior vena cava. Coil occlusion was performed on the abnormal artery arising from the infradiaphragmatic aorta. The patient was referred to surgery for repair of the anomalous pulmonary venous return and resection of the sequestered pulmonary segment.

Keywords: Infant, Scimitar syndrome

How to cite this article
Yakup Ergül, Kemal Nişli, Nermin Güler, Ümrah Aydoğan. A rare cause of recurrent wheezing and respiratory distress: Scimitar syndrome. Turk Kardiyol Dern Ars. 2011; 39(7): 595-598

Corresponding Author: Yakup Ergül, Türkiye
Manuscript Language: Turkish


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