ISSN 1016-5169 | E-ISSN 1308-4488
Archives of the Turkish Society of Cardiology
Pulmonary Hypertension Due to High-Output Heart Failure: Hereditary Hemorrhagic Telangiectasia [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. 2023; 51(7): 493-497 | DOI: 10.5543/tkda.2023.13614

Pulmonary Hypertension Due to High-Output Heart Failure: Hereditary Hemorrhagic Telangiectasia

Burçak Kılıçkıran Avcı1, Ali Uğur Soysal1, Emir Cerme2, Osman Aykan Kargın3, Ali İbrahim Hatemi2, Muhlis Cem Ar4, Zeki Öngen1
1Department of Cardiology, İstanbul University-Cerrahpaşa, Cerrahpaşa Faculty of Medicine, İstanbul, Türkiye
2Department of Internal Medicine, Division of Gastroenterology, İstanbul University-Cerrahpaşa, Cerrahpaşa Faculty of Medicine, İstanbul, Türkiye
3Department of Radiology, İstanbul University-Cerrahpaşa, Cerrahpaşa Faculty of Medicine, İstanbul, Türkiye
4Department of Internal Medicine, Division of Hematology, İstanbul University-Cerrahpaşa, Cerrahpaşa Faculty of Medicine, İstanbul, Türkiye

Pulmonary hypertension (PH) is a complex disorder that should be managed with a multidisciplinary approach. Although most of the underlying causes of left heart disease can be easily diagnosed with cardiac imaging, some pathologies might necessitate careful investigation to go beyond the obvious. High-output heart failure (HF) due to arteriovenous malformation (AVMs) is an unnoticeable cause for HF and PH. Patients with hepatic AVMs should always be carefully evaluated with regard to hereditary hemorrhagic telangiectasia (HHT) since they can have multiple signs related to the other systems without any symptoms. In this case report, we discussed a patient who was initially diagnosed as PH associated with HF with preserved ejection fraction but eventually was found to have PH associated with high-output HF due to hereditary hemorrhagic telangiectasia (HHT, or Osler Weber Rendu syndrome) after detailed evaluation.

Keywords: Bevacizumab, hereditary hemorrhagic telangiectasia, high-output heart failure, Osler Weber Rendu, pulmonary hypertension

How to cite this article
Burçak Kılıçkıran Avcı, Ali Uğur Soysal, Emir Cerme, Osman Aykan Kargın, Ali İbrahim Hatemi, Muhlis Cem Ar, Zeki Öngen. Pulmonary Hypertension Due to High-Output Heart Failure: Hereditary Hemorrhagic Telangiectasia. Turk Kardiyol Dern Ars. 2023; 51(7): 493-497

Corresponding Author: Burçak Kılıçkıran Avcı, Türkiye
Manuscript Language: English


Journal Metrics

Journal Citation Indicator: 0.18
CiteScore: 1.1
Source Normalized Impact
per Paper:
0.22
SCImago Journal Rank: 0.348

Quick Search



Copyright © 2024 Archives of the Turkish Society of Cardiology



Kare Publishing is a subsidiary of Kare Media.