Turk Kardiyol Dern Ars. 1997; 25(4): 252-254
A Case of Kearns-Sayre Syndrome with Atrioventricular block
Gülay AHUNBAY1, Ahmet ÇELEBİ1, İlknur ARSLANOĞLU1, Teoman ONAT1
A 14-year-old male patient diagnosed as Kearns-Sayre syndrome with chronic progressive external ophtalmoplegia, primary retinal degeneration and type I diabetes mellitus was hospitalized because of cardiac involvement. Having atrio-ventricular complete block permenant pacemaker was prophylactically, since the patient showed a rare mitochondrial myopathy, the case is presented and literatüre is reviewed.
Manuscript Language: Turkish