Double-orifice Mitral Valve Associated with Nonisolated Myocardial Noncompaction

Double-o rifice mitral valve is a rare congenital anoınaly . Although it is more frequently associated with other cardiac abnormalities, it may occur as an isolated lesion. There are two forms of ın yocardial noncompaction: isolated and non- isola ted myocardial noncompaction_ Nonisolated myocardial noncompactions are occasiona lly re ported postnatally in association with congenital heart anomalies such as VSDs, pulmonic stenosis, and ASDs. To our knowledge, this is the first case reporting a double orifice mitral valve associated with nonisolared myocardial noncompaction.