Libman - Sacks Endocarditis and Aneurysmatic Dilatation of the Ascending Aorta in Systemic Lupus Erythematosus of Childhood: Case Report*

erythematosus (SLE) is Libman-Sacks endocarditis characterised with noninfective valvular vegetations. Libman-Sacks endocarditis has been reported ve:ry rarely in paediatric lupus and as well as we know it has not been reported aneurysmatic dilatation of ascending aorta in SLE of children. 14 year-old giirl, whose symptoms and signs had begun at 4 years and she has been followed by the Paediatıric Rheumatology unit since 6 years-old, was referred to the Paediatric Cardiology unit for cardiac murmur. Echocardiographic evaluation was revealed valvular thickening and echodense vegetation on anterior leaflet of mitral valve with mild regurgitation, and valvular thickening and vegetation on right coroner cusp of the aortic valve with mild regurgitation. Additionally there was aneurysmatic dilatation of the ascending aorta without aortic stenosis. It is suggested that this vascular complication may be caused by the involvement of connective tissue of the vessel since she had not been hypertensive at ıthe time discovered the aneurism of ascending aorta.