Kearns-Sayre Syndrome: A case report

A case of Kearns-Sayre syndrome, a mitochondrial myopathy characterised by bilateral ptosis, chronic progressive external ophthalmoplegia, abnormal retinal pigmentation and cardiac conduction defects, was reported. The 22-year-old female patient was admitted to the hospital because of syncopal attack due to a highdegree AV block. Kearns-Sayre syndrome was diagnosed in her by clinical and laboratory examination. A permanent VVI pacemaker was implanted to the patient.