Archives of the
Turkish Society of Cardiology
Review - General

Pediatric pulmonary hypertension


Kolorado Çocuk Hastanesi, Çocuk Kardiyolojisi, Kolorado Üniversitesi Tıp Fakültesi, Aurora, Kolorado, ABD


Kolorado Çocuk Hastanesi, Çocuk Göğüs Hastalıkları, Kolorado Üniversitesi Tıp Fakültesi, Aurora, Kolorado, ABD


Columbia Üniversitesi, Doktor ve Cerrahlar Koleji, New York, New York, ABD


Konjenital Kalp Hastalıkları Merkezi, Çocuk Kardiyolojisi, Beatrix Çocuk Hastanesi, Groningen Üniversitesi, Groningen Üniversitesi Tıp Merkezi, Groningen, Hollanda


Necker Hasta Çocuk Hastanesi, Centre de Référence Malformations Cardiaques Congénitales Complexes (APHP), Çocuk Kardiyolojisi, Paris Dekart Üniversitesi, Paris, Fransa


Washington Üniversitesi, Biyoistatistik Anabilim Dalı, Seattle, Washington, ABD


Büyük Ormond Caddesi Hastanesi, Londra, İngiltere


Chicago İllinois Üniversitesi, Çocuk Hastalıkları Anabilim Dalı, Chicago, Illinois, ABD


Kaliforniya Üniversitesi Davis Çocuk Hastanesi, Çocuk Hastalıkları Kliniği, Davis, Kaliforniya, ABD


Üniversite Hastanesi, Çocuk Kardiyolojisi Birimi, Cenevre, İsviçre

Archives of the Turkish Society of Cardiology 2014; 42: Supplement 153-164
Read: 304 Downloads: 90 Published: 01 July 2021

Pulmonary hypertension (PH) is a rare disease in newborns, infants, and children that is associated with significant morbidity and mortality. In the majority of pediatric patients, PH is idiopathic or associated with congenital heart disease and rarely is associated with other conditions such as connective tissue or thromboembolic disease. Incidence data from the Netherlands has revealed an annual incidence and point prevalence of 0.7 and 4.4 for idiopathic pulmonary arterial hypertension and 2.2 and 15.6 for pulmonary arterial hypertension, respectively, associated with congenital heart disease (CHD) cases per million children. The updated Nice classification for PH has been enhanced to include a greater depth of CHD and emphasizes persistent PH of the newborn and developmental lung diseases, such as bronchopulmonary dysplasia and congenital diaphragmatic hernia. The management of pediatric PH remains challenging because treatment decisions continue to depend largely on results from evidence based adult studies and the clinical experience of pediatric experts. (J Am Coll Cardiol 2013;62: D117–26) ©2013 by the American College of Cardiology Foundation.

ISSN 1016-5169 EISSN 1308-4488