Turk Kardiyol Dern Ars. Ahead of Print: TKDA-65960 | DOI: 10.5543/tkda.2018.65960
Early and mid-term outcomes after surgical repair of congenital supravalvular aortic stenosis by Doty technique
, Muhammet Akyüz1
, Engin Karakuş1
, Esra Işık2
, Mehmet Fatih Ayık1
, Ertürk Levent3
, Yüksel Atay11
Ege University Faculty of Medicine, Department of Cardiovascular Surgery, Izmir, Turkey2
Ege University Faculty of Medicine, Department of Pediatric Genetics, Izmir, Turkey3
Ege University Faculty of Medicine, Department of Pediatric Cardiology, Izmir, Turkey
AIM To evaluate the efficacy, safety, early and mid-term outcomes of Doty surgical approach in pediatric patients with congenital supravalvular aortic stenosis.Keywords:
METHOD In our clinic, surgical repair with Doty technique has been performed to a total of 10 pediatric patients with supravalvular aortic stenosis between January 2005 and July 2015. These patients were evaluated retrospectively. Demographical characteristics, echocardiographic findings and clinical outcomes were analyzed.
RESULTS The mean age was 4.8 ± 3.9 years. Williams-Beuren syndrome was diagnosed in 4 of the patients. Early mortality was detected in one patient with diffuse supravalvular aortic stenosis. At the final follow-up (mean follow-up, 3.7 ± 1.2 years; range, 6-61 months), echocardiograms revealed the mean pressure gradient of 14 ± 4.2 mmHg. The two patients had minimal aortic insufficiency during follow-up period. No reoperation or reintervention was required.
CONCLUSION The Doty technique is anatomically and technically an effective surgical approach.
supravalvular aortic stenosis, Williams-Beuren syndrome, Doty technique
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Corresponding Author: Muhammet Akyüz, Türkiye