Archives of the Turkish Society of Cardiology
Early and mid-term outcomes after surgical repair of congenital supravalvular aortic stenosis by Doty technique [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. Ahead of Print: TKDA-65960 | DOI: 10.5543/tkda.2018.65960

Early and mid-term outcomes after surgical repair of congenital supravalvular aortic stenosis by Doty technique

Onur Işık1, Muhammet Akyüz1, Engin Karakuş1, Esra Işık2, Mehmet Fatih Ayık1, Ertürk Levent3, Yüksel Atay1
1Ege University Faculty of Medicine, Department of Cardiovascular Surgery, Izmir, Turkey
2Ege University Faculty of Medicine, Department of Pediatric Genetics, Izmir, Turkey
3Ege University Faculty of Medicine, Department of Pediatric Cardiology, Izmir, Turkey

AIM
To evaluate the efficacy, safety, early and mid-term outcomes of Doty surgical approach in pediatric patients with congenital supravalvular aortic stenosis.
Material and
METHOD
In our clinic, surgical repair with Doty technique has been performed to a total of 10 pediatric patients with supravalvular aortic stenosis between January 2005 and July 2015. These patients were evaluated retrospectively. Demographical characteristics, echocardiographic findings and clinical outcomes were analyzed.

RESULTS
The mean age was 4.8 ± 3.9 years. Williams-Beuren syndrome was diagnosed in 4 of the patients. Early mortality was detected in one patient with diffuse supravalvular aortic stenosis. At the final follow-up (mean follow-up, 3.7 ± 1.2 years; range, 6-61 months), echocardiograms revealed the mean pressure gradient of 14 ± 4.2 mmHg. The two patients had minimal aortic insufficiency during follow-up period. No reoperation or reintervention was required.

CONCLUSION
The Doty technique is anatomically and technically an effective surgical approach.

Keywords: supravalvular aortic stenosis, Williams-Beuren syndrome, Doty technique

How to cite this article


Corresponding Author: Muhammet Akyüz, Türkiye
© Copyright 2018 Archives of the Turkish Society of Cardiology
LookUs & Online Makale