Case Report and The Surgical Treatments of Two Cases with Pulmonary Atresia in which Pulmonary Arteries is Circulated by Coronary Arteries [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. Ahead of Print: TKDA-98047 | DOI: 10.5543/tkda.2017.98047

Case Report and The Surgical Treatments of Two Cases with Pulmonary Atresia in which Pulmonary Arteries is Circulated by Coronary Arteries

Kahraman Yakut1, Kursad Tokel1, Birgul Varan1, Ilkay Erdogan1, Murat Ozkan2
1Baskent University, Department of Pediatric Cardiology, Ankara
2Baskent University, Department of Cardiovascular Surgery, Ankara

Pulmonary atresia, together with the ventricular septal defect can be seen in a wide spectrum like from a simple valve atresia to a condition where pulmonary bed is circulated by collateral arteries separated from the aorta and there is no real pulmonary arteries or present but hypoplastic. The size of the pulmonary arteries and concomitant complex cardiac lesions are important in deciding treatment method and all the correctional alternatives. While complete correction surgeries in tetralogy of Fallot correction style is done in simple forms, too many invasive procedures are done to the patients on the other side of the spectrum and the quality of life is very variable. The size of the pulmonary artery and its branches, the presence of the accompanying collateral vessels, is the determining factor in the management of the disease. In this case report, we wanted to introduce two patients, one of which was the first case was 40 days and the second case was two days old diagnosed with VSD, pulmonary atresia where the circulation of pulmonary arteries were from coronary arteries by the help of echocardiography performed after murmurs heard while examination. In our second case, diagnosis was confirmed by catheter angiography, and in our first case the final diagnosis could be made during surgery. The aim in reporting this case is to emphasize the importance of the pulmonary artery size, presence of pulmonary confluence, where the circulation comes from and concomitant collateral arteries, in treatment methods.

Keywords: Congenital heart disease, pulmonary atresia, coronary artery, surgical treatment.

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Corresponding Author: Kahraman Yakut, Türkiye
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