Turk Kardiyol Dern Ars. 2018; 46(5): 385-391 | DOI: 10.5543/tkda.2018.65960
Early and mid-term outcomes after surgical repair of congenital supravalvular aortic stenosis with the Doty technique
, Muhammet Akyüz1
, Engin Karakuş1
, Esra Işık2
, Mehmet Fatih Ayık1
, Ertürk Levent3
, Yüksel Atay11
Department of Cardiovascular Surgery, Ege University Faculty of Medicine, İzmir, Turkey2
Department of Pediatric Genetics, Ege University Faculty of Medicine, İzmir, Turkey3
Department of Pediatric Cardiology, Ege University Faculty of Medicine, İzmir, Turkey
OBJECTIVE The aim of this study was to evaluate the efficacy and safety of the Doty surgical approach in pediatric patients with congenital supravalvular aortic stenosis (SVAS) by examining early and mid-term outcomes.
METHODS Surgical repair using the Doty technique was performed in a total of 10 pediatric patients with SVAS between January 2005 and July 2015 at this clinic. These patients were evaluated retrospectively. Demographic characteristics, echocardiographic findings, and clinical outcomes were analyzed.
RESULTS The mean patient age was 4.8±3.9 years. Williams-Beuren syndrome was diagnosed in 4 of the patients. Early mortality was observed in 1 patient with diffuse SVAS. At the final follow-up (mean follow-up: 3.7±1.2 years; range: 6-61 months), echocardiograms revealed a mean pressure gradient of 14±4.2 mmHg. Two patients displayed minimal aortic insufficiency during the follow-up period. No reoperation or reintervention was required.
CONCLUSION The Doty technique is an anatomically and technically effective surgical approach to treating SVAS.
Doty technique, supravalvular aortic stenosis; Williams-Beuren syndrome.
How to cite this article
Onur Işık, Muhammet Akyüz, Engin Karakuş, Esra Işık, Mehmet Fatih Ayık, Ertürk Levent, Yüksel Atay. Early and mid-term outcomes after surgical repair of congenital supravalvular aortic stenosis with the Doty technique. Turk Kardiyol Dern Ars. 2018; 46(5): 385-391
Corresponding Author: Muhammet Akyüz, Türkiye