Right atrial myxoma associated with portal and splenic vein thrombosis in a patient with Budd-Chiari syndrome [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. 2011; 39(4): 320-324 | DOI: 10.5543/tkda.2011.01329

Right atrial myxoma associated with portal and splenic vein thrombosis in a patient with Budd-Chiari syndrome

Burak Onan, Zehra Bayramoğlu, İsmihan Selen Onan, Belhhan Akpınar
Department of Cardiovascular Surgery, Florence Nightingale Hospital, Istanbul, Turkey

Budd-Chiari syndrome (BCS) is a rare disorder characterized by hepatic venous obstruction. A 41-year-old male patient presented with right upper quadrant pain, abdominal distension, and dyspnea. He had a history of BCS that was associated with polycythemia vera. Abdominal computed tomography showed hepatomegaly and a hypodense filling defect suggestive of thrombus formation in the hepatic, splenic, and portal veins, and suprahepatic part of the inferior vena cava. Transthoracic echocardiography performed to assess the extension of this pathological process and its relation with intracardiac structures showed a mass lesion in the right atrium, about 4x3 cm in diameter. The lesion manifested as an intracardiac thrombus extending from the inferior vena cava. The patient underwent surgical treatment to remove the atrial mass. At surgery, the lesion turned out to be an atrial tumor, which was diagnosed as atrial myxoma in histopathologic examination. The symptoms of the patient resolved after surgery.

Keywords: Budd-Chiari syndrome/etiology, echocardiography, heart atria/pathology, myxoma/complications/surgery; venous thrombosis/etiology

How to cite this article
Burak Onan, Zehra Bayramoğlu, İsmihan Selen Onan, Belhhan Akpınar. Right atrial myxoma associated with portal and splenic vein thrombosis in a patient with Budd-Chiari syndrome. Turk Kardiyol Dern Ars. 2011; 39(4): 320-324

Corresponding Author: Burak Onan, Türkiye
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